Imaging Findings of Osler - Weber - Rendu Disease Involving the Liver

Osler -Weber -Rendu disease or hereditary hemorrhagic telangiectasia(HHT) has been known to be an autosomal dominant disorder characterized by telangiectases and arteriovenous malformations of multiple organ systems(1). Hepatic involvement occurs in 8-31 % ofcases with HHTand includes telangiectases or arteriovenous fistulas associated with fibrosis and cirrhosis(2 , 3). Recent reports demonstrate various imaging findings including Doppler sonography with color flow signals , CT, and MR findings of the liver involvement in patients with HHT(2 -4). A few cases with HHT had reported in Korea(5). We describe the findings of conventional and Doppler sonography, and computed tomogram(CT) in a case with HHT involving the liver